discussions in

anterior segment disease

ALAN G. KABAT, OD, FAAO

MEMPHIS, TN

JOSEPH SOWKA, OD, FAAO ANDREW GURWOOD, OD, FAAO

FT. LAUDERDALE, FL PHILADELPHIA, PA

Course Description: Case presentations provide a springboard for in-depth discussion of several challenging anterior segment conditions. Emphasis is placed on understanding the presentation, pathophysiology and management of the various clinical entities.

Learning Objectives/Outcomes: At the conclusion of this course, the attendee will be able to:

1.  Identify the pathophysiology, clinical presentation and management of bacterial keratitis;

2.  Identify the pathophysiology, clinical presentation and management of dacryoadenitis;

3.  Identify the pathophysiology, clinical presentation and management of corneal laceration;

4.  Identify the pathophysiology, clinical presentation and management of uveitis, as well as the essential laboratory work up;

5.  Identify the pathophysiology, clinical presentation and management of herpes simplex keratitis;

6.  Identify the pathophysiology, clinical presentation and management of recurrent corneal erosion.

BACTERIAL KERATITIS

·  Breakdown of corneal defenses (dry eyes, corneal trauma, corneal hypoxia, etc.)

·  Introduction of pathogen (corneal abrasion mismanagement, contact lenses, etc.)

·  Proliferation of organisms and release of toxins and proteolytic enzymes

·  Antigen-antibody reaction

·  Stromal edema (splitting of stromal collagen lamellae sheets)

·  Cellular transudation and emigration

·  Infiltration

·  Phagocytosis of organisms with proteolytic enzyme release and stromal lysis

·  Antigenic neutralization (hopefully)

·  Cicatrization (fibroblastic proliferation of scar tissue)

·  Visual loss

Clinical Picture of Bacterial Keratitis

·  Pain, photophobia, lacrimation

·  Profound conjunctival and episcleral injection

·  Involvement of innocent bystanding tissue

·  Anterior chamber reaction

·  Possible (sterile) hypopyon

·  Focal infiltrate with overlying epithelial staining and breakdown

·  The spectrum of clinical findings is broad (from an initially mild, often misdiagnosed presentation of S. aureus to the exaggerated presentation of Pseudomonas)

-  Any staining infiltrate should be presumed to be an infectious ulcer until proven otherwise

Management of Bacterial Keratitis

·  Cultures and sensitivity studies

·  Broad spectrum antibiosis: Fluoroquinolones

1.  Ciprofloxacin (Ciloxan) ii gtt Q15min X 6hrs, then ii gtt Q 30min X 18 hrs.

2.  Ocuflox Q30 minutes while awake, and then BID at night is as effective as fortified antibiotics.

3.  Levofloxacin (Quixin)?

4.  New alternatives- fourth generation fluoroquinolones: Vigamox/ Moxeza (moxafloxacin); Zymar/ Zymaxid (gatifloxacin) – Q1H

·  Equal gram (-) coverage, greater gram (+) coverage than earlier generation fluoroquinolones

5.  Newest options: Besivance (besifloxacin), Moxeza (moxifloxacin), Zymaxid (gatifloxacin)

·  Cycloplegics (scopolamine 0.25% TID or atropine 1% BID) - decreases blood-aqueous barrier breakdown

·  Corticosteroids (reduces inflammation by constricting blood vessel walls and reducing vessel wall permeability. Also blocks prostaglandin formation and release and stabilizes lysosomal membranes).

·  Use corticosteroids only if step 1 is successfully completed (clinical impressions vs. microbiologic study results).

DACRYOADENITIS

·  Inflammation of the lacrimal gland

·  Usually seen in younger adults

·  May be acute or chronic:

o  Acute form presents with greater pain, redness & symptomology; usually infectious in nature (bacterial or viral)

o  Chronic form is more common; usually inflammatory & due to underlying systemic autoimmune disease (e.g. sarcoidosis, Sjögren's syndrome, systemic lupus erythematosus, Wegener's granulomatosus)

·  Acute Dacryoadenitis -

o  Typically unilateral

o  Ocular redness, tearing, & swelling of the upper lid

o  Painful proptosis & ophthalmoparesis

o  May have associated preauricular lymphadenopathy & fever

·  Chronic Dacryoadenitis -

o  Usually bilateral

o  S-shaped swelling to outer ⅓ of the eyelid

o  Pain is variable

o  Swollen lacrimal gland is often evident on lid retraction

·  Dacryoadenitis: Diagnostic management

o  Orbital CT or MRI

o  Laboratory studies

o  CBC with differential

o  Serology based on history & associated symptoms (e.g. ACE, FTA-ABS, RPR, PPD with anergy panel)

o  Transcutaneous, transeptal biopsy should be performed in recalcitrant cases of dacryoadenitis or when a malignant process is suspected

·  Dacryoadenitis: Therapeutic Management

o  Acute - warrants systemic antibiotics

§  Amoxicillin (250-500 mg po q8h)

§  Cephalexin (250-500 mg po q6h)

§  In more severe cases, hospitalization with IV antibiotics may be necessary

o  Chronic dacryoadenitis may be managed with a course of systemic steroids

§  Typical therapy involves 80-100 mg of oral prednisone daily for 1-2 weeks, followed by slow taper.

PENETRATING INJURY: CORNEAL LACERATION

·  Excessive PAIN, decreased vision

·  Deeper than abrasion; may be smaller, linear

·  + Seidel’s sign; additionally, may see hyphema, A/C rxn, flattened A/C (relative), air bubbles in A/C

·  Iris prolapse possible

·  IOP is low -- DO NOT perform tonometry!

·  Management

o  Photodocument (if possible for clinicolegal purposes)

o  MINIMAL manipulation of the globe!

o  Avoid topical medications!

o  Shield the eye but DO NOT PATCH!

o  N.P.O.

o  Refer IMMEDIATELY for surgical repair

ANTERIOR UVEITIS

·  Associated factors

o  An inflammation of the iris and ciliary body

o  May result from direct trauma to the eye (most often)

o  May occur as a result of inflammation of other ocular structures (e.g., keratitis, scleritis)

o  May be associated with underlying systemic disease (including but not limited to):

§  ankylosing spondylitis

§  Behçet’s disease

§  inflammatory bowel disease

§  juvenile rheumatoid arthritis

§  Reiter’s syndrome

§  sarcoidosis

§  syphilis

§  tuberculosis

§  Lyme disease

o  Improper management may result in secondary, inflammatory glaucoma

·  Signs and Symptoms

o  Signs:

§  Variable redness

§  Ptosis or blepharospasm (due to discomfort)

§  Tearing

§  Visual acuity normal to mildly reduced

-  20/40 or better in most cases

-  More difficulty with near / accommodative tasks

o  Symptoms:

§  Deep, dull “achy” pain in affected eye and orbit

§  Extreme photophobia

§  “Hazy” vision

§ 

·  Biomicroscopic evaluation

o  Mild lid congestion (pseudoptosis); palpebral conjunctiva is unaffected

o  Circumlimbal “flush” , i.e., injection of the episclera and conjunctiva concentrated around the cornea

o  Mild corneal edema

o  Keratic precipitates in chronic conditions (“granulomatous”)

o  Anterior chamber “cells & flare” **

§  “cells” = white blood cells liberated from uveal blood vessels

§  “flare” = proteinaceous by-products of inflammation

o  Posterior or (less commonly) anterior synechia

o  Iris nodules

o  Altered intraocular pressure

§  Initially reduced because of secretory hypotony

§  Inflammatory by-products clog the trabecular meshwork, inducing IOP elevation

§  May range from 30 to 80 mmHg in extreme cases

·  Management

o  2 primary goals:

1.  immobilize the iris & ciliary body to decrease pain and prevent exacerbation

2.  quell the inflammatory response to prevent ocular sequelae

o  STRONG topical cycloplegics

§  Choice of drug dependent upon severity of reaction, iris color, and presumed patient compliance

§  Best choices include

-  ¼% scopolamine

-  1% atropine

o  Topical corticosteroids

§  Must be deeply penetrating and efficacious

§  Must be given FREQUENTLY, particularly during early stages of treatment

§  Drug choices include:

-  difluprednate **

-  prednisolone acetate

-  loteprednol ?

o  Address synechiae using 1% atropine + 10% phenylephrine topically

o  Elevated IOP should be addressed using standard topical antiglaucoma therapy:

§  b-blockers (e.g., TimopticÒ, BetopticÒ)

§  CAIs (e.g., TrusoptÒ)

§  Prostaglandin analogs (e.g., XalatanÒ) offer no clinical benefit

§  Miotics (e.g., pilocarpine) are ABSOLUTELY CONTRAINDICATED

o  In recurrent cases (i.e., two or more similar presentations), a thorough medical evaluation to ascertain underlying etiology is indicated

§  CXR

§  Sacroiliac joint films

§  Serology:

-  CBC with differential

-  ESR

-  ANA

-  HLA-B27

-  RF

-  ACE

-  FTA-ABS

-  Lyme titer

Herpes Simplex Keratitis

·  Pathophysiology:

-  Initial infection by herpes simplex virus occurs in childhood (hand to eye, mouth to eye)

-  After initial infection, virus enters a dormant phase in cell ganglia

§  "Trigger factors" induce reactivation of viral replication throughout the patient's life; include: fever, emotional stress, exposure to UV radiation, menstruation, trauma, immunosuppression

§  About half of all infected patients experience re-activation within 5 years

§  Most commonly ocular manifestion is dendritic epithelial keratitis

§  More severe presentations can manifest as geographic epithelial keratitis

·  Clinical presentation - dendritic keratitis:

-  Branching epithelial ulcer; may begin as nondescript punctate epitheliopathy

-  Stains centrally with NaFl, peripherally with rose bengal or lissamine green ("terminal end-bulbs")

-  Associated conjunctival injection, edema; uveitis possible

-  Recurrent attacks lead to corneal hypoesthesia, i.e. diminished corneal sensitivity

§  (+) Cotton-wisp test

§  Patients may be far less symptomatic than predicted by ocular appearance

·  Management:

-  Herpes virus cannot be eradicated; management efforts are aimed at suppression and amelioration of symptoms

-  Historical tandard of care in U.S. is topical trifluridine 1% q2h - 9 times daily, tapered to q3-4h as ulcer shows signs of closure; maintain at QID for at least 7-10 days.

-  More recent option is ganciclovir 0.15% ophthalmic gel 5 times daily until resolution, then reduced to TID for 7 days

-  Oral acyclovir may be used in patients who lack dexterity or compliance with topicals (400 mg po five times daily)

-  Corticosteroids are absolutely contraindicated in active epithelial infection

-  Herpetic Eye Disease Study (HEDS) 1998: Acyclovir 400 mg po BID X 12 months may reduce rate of recurrence by as much as 50%

RECURRENT CORNEAL EROSION

·  History, History, History

-  History of Corneal Abrasion

-  Previous episodes of RCE

-  Pain on awakening

·  A breakdown of the epithelial layer of the cornea due to a breach in the integrity of the basement membrane

·  Common Etiologies:

-  Corneal dystrophy (e.g. granular dystrophy)

-  Trauma; often follows improperly treated corneal abrasion

·  Can present as a small epithelial defect or as a large abrasion

·  Treatment

-  Bandage SCL

§  Pressure patching in rare instances

-  Prophylactic ntibiotic

-  Cycloplegic

-  Artificial Tears and Hypertonic agents

-  Anterior Stromal Puncture (ASP)

-  Oral doxycycline + topical steroids

-  Amniotic membrane… ?